Sirarat Sarntivijai

MedDRA:10034280

NCIT:C34909

SCTID:65172003

ICD10CM:L10

UMLS:C0030807

MESH:D010392

MeSH:D010392

DOID:9182

ICD9:694.4

MONDO:0006594

ICD10:L10

Wikipedia:Pemphigus

NCIt:C34909

Pemphigus is a group of chronic autoimmune skin diseases characterised by blisters formation on the outer layer of the skin and the mucous membranes. Three clinical forms have been characterised, of which paraneoplastic pemphigus is extremely rare. [ Orphanet:63455 ]

a rare group of blistering autoimmune diseases that affect the skin and mucous membranes.

Pemphigus is a group of rare autoimmune diseases that cause blistering of the skin and mucous membranes (mouth, nose, throat, eyes, and genitals).This conditioncan occur at any age, but often strikes people in middle or older age. Studies have shown that some populations may be at greater risk for certain types of pemphigus. For instance, people of Jewish descent and those from India, Southeast Europe, and the Middle East are at greater risk for pemphigus vulargis, while pemphigus foliaceus is more common in North America, Turkey, and South America. Pemphigus is a chronic disease which is best controlled by early diagnosis and treatment.Treatment includes steroids to reduce inflammation,drugs that suppress the immune system responseand antibiotics to treat associated infections. There are four main types of pemphigus: Pemphigus vulgaris Pemphigus foliaceus IgA pemphigus Paraneoplastic pemphigus

EFO:1000749

pemphigus

Sirarat Sarntivijai

EFO:1000749

pemphigus